BopheloMafu a le Maemo

Gardner lefu ke eng?

Ho na le pathologies tse ngata tseo ba li futsitseng, 'me ba beha boemong ba liphatsa tsa lefutso. Leha ho le joalo, tse ling tsa tsona li sa hang-hang, empa feela ka batho ba baholo. Har'a mafu joalo Gardner lefu. bolwetse Sena se bolela ho lihlahala nang kotsi, ka linako tse ling e na le tšekamelo ea ho ba malignancy, ke hore, e tsoela ka kankere.

Tlhaloso Gardner syndrome,

bolwetse ena e ho ke ho tsejoe tsoa. E ile ea pele o ile a hlalosa lilemong tsa bo-bohareng ba bo-bo20 la lilemo, bo-rasaense ba Gardner. E ne e le eena ea ileng a se tiisitsoeng sehokelo lipakeng tsa lihlopha nang kotsi ea letlalo la, masapo, 'me pampitšana tshilong ya dijo. lebitso le leng la lefu lena le - e ke lelapa (kapa lefa) adenomatous polyposis. lefu Gardner ke tšabehang e seng feela tse ngata setlolo likoli letlalo. Ho lumeloa hore polyposis mala fetoha mofuta o bolaeang ka 90-95% ea linyeoe. Ka lebaka lena, ka bolwetse ho nkoa hore tlama diso precancerous. The tepelletse maikutlong differential o etsoang tsoa le atheroma lefu Riklenghauzena, osteomas le 'ngoe le polyps mala.

Lisosa tsa lefu lena le mochine oa ntshetsopeleng

lefu Gardner e bua ka bolwetse lefa. Ho e fetisoa liphatsa tsa lefutso ho batsoali ba le litho tse ling tsa lelapa (batsoali). mofuta oa lefa la lefu lena le - autosomal ka sehloohong. Sena se bolela e le kgonego phahameng tsa phetiso ea lefu ho batsoali ba bana ba. Ka pelo ea Gardner mochine lefu ntshetsopeleng e dysplasia mesenchyme. Ka lebaka la lesela ena e thehoa ka letlalo la, lesapo le mucosa pampitšaneng ena gastrointestinal, ho na le tšobotsi e hlaheletseng ea lefu lena le setshwantsho litleleniki tsa. Ho phaella ho liphatsa tsa lefutso predisposition mesenchymal dysplasia ka thehoa le tlas'a tšusumetso ea lintlha tse kotsi amang ntshetsopeleng prenatal nako ya trimester pele ea bokhachane.

lefu Gardner e reng: matšoao a

Hangata ka ho fetisisa, le maloetse o bontša ka boeona e ka ba mocha (lilemo tse 10). Maemong a mang, matšoao a pele qala hamorao - se bophelong batho ba baholo. lefu Gardner e na le liphello tse latelang: ke lihlahala letlalo, bonolo dinama tse nyenyane tse, lesapo le tsamaiso tshilong ya dijo. Ho phaella ho polyps mala a ka hlaha ka mpeng le duodenum. Ka letlalo ka ho ketekoa atheroma, dermoid le cysts sebaceous, fibroids. Hape, hoa khoneha ho hlaha ha nang kotsi dinama tse nyenyane tse le bonolo. Tsena li akarelletsa lipoma le leiomyoma. lihlahala tsena tsohle ka etsahala ka sefahleho sa, letlalo la hlooho, matsoho kapa maoto. Ho phaella tabeng ea ho na le diso masapo. Ba ile ba boela ba ea nang kotsi, empa hangata ho thata ho mosebetsi. Mohlala, osteoma le lesapo la mohlahare tlaase, lehata. sekame tsena kena-kenana hlafuna le ka hatella sebopeho boko. Ponahatso fetisisa e mpe ea lefu lena le ke mantle a polyps le pampitšana e meng tshilong ya dijo. Maemong a mangata, lihlahala tsa tshilong ya dijo pampitšana mucous lera la maligniziruyutsya, ke hore, fetoha kankere. Polyps a ka ba le nako e telele ho se utloa. Hangata ka ho fetisisa, bakuli ba tletleba la mathata, mala obstruction, tsoa mali.

Gardner syndrome, kalafo ka Cuba: melemo

Ho tloha ka lefu lena le ke precancer tlama hloka ho tlosa ho buoa ea dihlahala. Ho bohlokoa ho hlahloba lefu Gardner e. Photo bakuli ka bonoa lingoliloeng tse kankere, kapa libaka khethehileng. Ho phaella ho ponahalo ea tleleniki ke ho hlokahala hore ho tsamaisa radiography tsa pampitšana tshilong ya dijo, colonoscopy. Letlalo diso le polyposis mala lumella tepelletse maikutlong nepahetse. Gardner syndrome, kalafo o etsoang tsoa linaheng tse ngata. Melemo ea litleliniking ba Cuba kenyeletsa thepa ea morao-rao, litsenyehelo tsa ho etsa liopereishene ho buoa, haholo profesionalce ba tšoanelehang ba tsoang likarolong tsohle tsa lefatše. The kalafo ke ho tlosa karolo anngoeng ke likoluoa tsa mantle a ka. U ka boela tlosa likoli setlolo letlalo.

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