Ectodermal le fibrous dysplasia. liphio dysplasia

Tlas'a dysplasia (fetoletsoe ho tloha Segerike e le dys - latola; wplasis - thuto) le bolela se fosahetseng le ho khopamisa ntshetsopele ya lekala le teng. Sena ke - e leng lentsoe le kopanetsweng koahela ditlolo efe kapa efe.

Fibrous dysplasia bua ka mafu a ea tsamaiso ya marapo, 'me e tšoauoa ka hore lesapo dinama tse nyenyane tse e nkeloa sebaka ke dinama tse nyenyane tse fibrous. Tshebetso ena deforms masapong. Sesosa se ka sehloohong sa lefu lena ke ponahalo ea thulaganyou e hlahala, e qala ka ngoana ho, 'me joale e qala ho hatela pele. Fibrous dysplasia hangata ka basali.

lefu 'maloa classifications. Unit atileng ka ho fetisisa ke, ho itšetlehile ka boemo ba keketseho ea tshebetso pathological:

• monoossalnaya fibrous dysplasia ama feela lesapo le leng;
• poliossalnaya - liphetoho tse hlokometse masapong a mangata (hangata ata ka lehlakoreng le leng ea 'mele,' me hangata le hlaha ka bongoaneng).

Mofuta oa pele oa lefu lena le ama lesapo cranial, lehare, masapo tubular (telele) bohale. Ea bobeli - ka nako e tšoanang ba etsang liphesente tse fetang mashome a mahlano tsa masapo kaofela masapo le.

The mathata a ka sehloohong a akarelletsa fractures khafetsa, e leng se ka potlako coalesce, empa khatello ntlafatsoa ka masapo, hammoho le sarcoma.

Fibrous dysplasia ho kalafo efe kapa efe a ke ke a ba teng, ka mekgwa ya tshebetso feela masapo (transplant lesapo curettage, osteotomy), 'me ha ho khethoa lithethefatsi hore lopollang bohloko.

Ectodermal dysplasia akarelletsa palo e khōlō ea mafu a le syndromes (ka 100), ha e le hantle ba tse ke ho ba teng ha e sa tloaelehang ntshetsopeleng ya derivatives ectoderm. Ha ba qala - ho ba teng ha hyperthermia, eo ha a bolela hore le litlhaselo tse etsoang khafetsa ho ka etsa hore le boo ho hōla efe kapa efe ea kelello, kapa lefu.

O ka khetha mefuta e latelang 'me matšoao a bona.

Angidroticheskaya qala ho iponahatsa ka masea, le moshanyana 'me a ntse a tsoela pele ho pholletsa le bophelo. Likarolo ya sehlooho ke ena:

• mafu a lefa;
• deformation matla tsa meno le;
• ho ba teng ha ka slowdown ka lipekere e;
• mucosal felloa ke matla (metso, molomo, nko);
• ponahalo Link e tšoanang le ea bakuli ba ngoana le congenital mokaola.

kalafo bontshang matshwao fuoang. Thibetsoe: matsatsi a phomolo a linaheng tse ka boroa, mosebetsi oa ho chesa le lik'hemik'hale limela.

Gidroticheskaya ekzodermalnaya dysplasia e tšoauoa ka liphetoho tse ka liatla ka, bohato, moriri ntshetsopele. Ka kalafo e hangata laolwa vithamine "A" ka ntle le ka hare, softening tranelate le keratolytics. Ho phaella ho sena, sebelisa: enzymatic bolela Methyluracilum, anabolic steroid, zinki-amino acid le biostimulants.

Renal dysplasia na le mefuta e 'maloa eo e fapana:

• liponahatso morphological (cystic le e bonolo);
• Diriswa (cortico-medullary, medullary le cortical);
• ata - palo yohle, segmental, tsepamiso).

Sesosa se ka sehloohong sa lefu lena ho na le mabaka liphatsa tsa lefutso le ho teratogenic hare le kantle tšusumetso e ka embryo. Ka hona, ka lebaka la lefu lena le ke congenital malformations, eo, ho sa tsotellehe mofuta wa, etsa hore motho a fokotseha ka boholo a liphio, sehlōhō ntshetsopeleng ya parenchyma, phokotso e khōlō ea mesebetsi ea eona.

Kalafo ea lefu lena ke bontshang matshwao le khafetsa Maemong a ha ho na sesupo bakeng sa transplantation ea lekala e.

Ka kakaretso, dysplasia kenyelletsa ditokiseletso sehlopha sa mafu tseo kenyeletsa e sa tloaelehang ntshetsopeleng ya makala kapa tsamaiso eohle. E le busa, ba ka sehloohong e bakang - lintlha liphatsa tsa lefutso le ho congenital.

Phekolo e bontshang matshwao, kapa dikgothaletso ke bakeng sa transplant lekala kapa lesapo.